Name: Congenital FXIII deficiency in southern Tunisia (en Inglés)
Price: 355068.00 COP
Availability: InStock
Author: Krichen, Imen ; Frikha, Imen ; Kallel, Choumous
ISBN: 9786205914564

portada Congenital FXIII deficiency in southern Tunisia (en Inglés)

Formato

Libro Físico

Autor

Choumous Kallel

Imen Krichen

Imen Frikha

Editorial

Our Knowledge Publishing

Idioma

Inglés

N° páginas

Encuadernación

Tapa Blanda

Dimensiones

22.9 x 15.2 x 0.5 cm

Peso

0.14 kg.

ISBN13

9786205914564

Categorías

Cuestiones generales de la medicina

Congenital FXIII deficiency in southern Tunisia (en Inglés)

Choumous Kallel (Autor) · Imen Krichen (Autor) · Imen Frikha (Autor) · Our Knowledge Publishing · Tapa Blanda

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Reseña del libro "Congenital FXIII deficiency in southern Tunisia (en Inglés)"

Congenital factor XIII deficiency is a rare coagulopathy whose prevalence in the world is of the order of one case per 2 million inhabitants. This study made it possible to list the cases of factor XIII deficiency in southern Tunisia and to evaluate the epidemiological, diagnostic and therapeutic aspects. Our study is retrospective, covering a period of 20 years and including 30 patients. A standard haemostasis work-up and factor XIII assay were performed in all our patients. The sex ratio was 0.67. The majority of patients were from Sidi Bouzid. The mean age of onset of symptoms was 1.4 years. The mean age at diagnosis was 8.8 years. 26 patients were diagnosed following a hemorrhagic syndrome and 4 following a family investigation. All had zero factor XIII levels, as measured by the clot solubility technique. All patients received replacement therapy with fresh frozen plasma. The majority of cases were from consanguineous marriages.Therefore, family investigations are of interest to obtain a better epidemiological and molecular profile.